This method avoids surgical procedure and associated risks cardiovascular debility due to anemia and iron overload 19 , 20 , However, suppression of bone marrow due to radiation may be observed in already anemic patients. In some patients whose surgery and radiation therapies may cause special risks e. This will especially be effective in patients presenting severe EMH Cord compression resulting from EMH is a rare complication in patients with thalassemia. An immediate therapy is necessary in the management of patients with cord compression and can result in promising response in different treatment modalities such as surgical decompression, radiation therapy and repeated blood transfusion.
However, the appropriate treatment of these patients depends on their status; hypertransfusion seems to be useful which can be regarded as a first-line treatment. Spinal cord compression due to extramedullary haematopoiesis in two patients with thalassaemia: complete regression with blood transfusion therapy.
J Neurol. Spinal extradural hematopoiesis in adolescents with thalassemia. Report of two cases and a review of the literature.
Childs Nerv Syst. Spinal cord compression secondary to extramedullary hematopoiesis in thalassemia intermedia. Eur Spine J.
Radiology of Thalassemia
Papavasiliou C. Tumor simulating intrathoracic extramedullary hematopoiesis. Incidence and clinical study of ectopic erythropoiesis in adult patients with thalassemia intermedia. Ann Ital Med Int. Cord compression due to extramedullary hemopoiesis in a patient with thalassemia. Spine Phila Pa Spinal cord compression due to extramedullary haematopoiesis in thalassaemia: a case report and review of the literature. Spinal cord compression secondary to extramedullary hematopoiesis in thalassemia.
Iran J Radiol. Spinal epidural extramedullary hematopoiesis with cord compression in a patient with refractory sideroblastic anemia. Case report. J Neurosurg. Paraplegia in a pregnant thalassemic woman due to extramedullary hematopoiesis: successful management with transfusions. Surg Neurol. Extramedullary hematopoiesis in thalassemia intermediate presenting as paraplegia. J Clin Neurosci. Pantongrag-Brown L, Suwanwela N. Case report: chronic spinal cord compression from extramedullary haematopoiesis in thalassaemia--MRI findings.
Spinal cord compression due to epidural extramedullary haematopoiesis in thalassaemia: MRI. MRI diagnosis of spinal cord compression in beta-thalassemia. CT and MRI of symptomatic spinal involvement by extramedullary haemopoiesis. A case of spinal cord compression by extramedullary haemopoiesis in a thalassaemic patient: a putative role for hydroxyurea? Combined radiotherapeutic and surgical management of a spinal cord compression by extramedullary hematopoiesis in a patient with hemoglobin E beta-thalassemia. Acta Haematol. Recurrence of spinal cord compression from extramedullary hematopoiesis in thalassemia intermedia treated with low doses of radiotherapy.
Am J Hematol. Extramedullary haematopoiesis in thalassaemia: results of radiotherapy: a report of three patients. Clin Oncol R Coll Radiol. The role of radiation therapy in the management of spinal cord compression due to extramedullary haematopoiesis in thalassaemia.
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J Neurol Neurosurg Psychiatry. Iranian Journal of Radiology: 9 3 ; Published Online: September 17, Received: June 18, Revised: May 21, Accepted: May 28, Note the cortical erosions arrow and thickening of residual trabeculae.
Learning objectives 1 to understand the different manifestations of thalassemias, 2 to illustrate the skeletal and non-skeletal features of thalassemias through an iconography of our own practice in order to highlight the contribution of imaging to their diagnosis. Read more. They were first described by Cooley et al. In all thalassemias, clinical features that result from anemia, transfusional, and absorptive iron overload are similar but vary in severity Findings and procedure details We looked at the results of the different imaging modalities Xray, ultrasound, CT scan and MRI of patients with thalassemias and tried to use them to illustrate the skeletal and non-skeletal features of thalassemias.
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The skeletal system's response to this bone marrow proliferation consists of bone marrow Conclusion Manifestations of thalassemias are rich and variable. The choice of the modality is conditioned by the clinical examination. X-ray is generally adequate in defining osseous abnormalities. CT and MRI techniques can document the iron oveload, extramedullary hematopoiesis, and bone marrow changes. Personal information.
Am J Dis Child, ; Ben Brahim O, Ladeb S,. Bone mineral Jugovec , R.
Extramedullary hematopoiesis: findings on computed tomography scans of the chest in 6 patients
Garbajs, D. Petkovic , Z.
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